Phone 212-263-7951 Fax 212-263-0462
Francis V. Adams, M.D.
Francis V. Adams, M.D.

Cystic Fibrosis

Cystic fibrosis (CF) is a genetic disease affecting approximately 30,000 children and adults in the U.S. CF is chronic and progressive, and the disease causes mucus to become thick, dry, and sticky. The abnormally thick mucus builds up and clogs passages in many of the body's organs, mainly the lungs and the pancreas. People with CF have an average life expectancy of about 30 years.

In the lungs, CF can cause serious breathing problems and lung disease, including life-threatening lung infections. To dislodge the mucus, CF patients cough frequently and require time-consuming daily chest and back clapping and body positioning to drain lung secretions. Frequent infections and the resulting inflammation gradually damage the lungs, causing respiratory failure, which is the leading cause of death among people with CF.
recommended reading
These articles provide in-depth information and are written to help you make the best healthcare decisions for you and your loved ones.
Cystic Fibrosis

action sets
Action Sets are designed to help you take an active role in managing a health condition. Action Sets provide the tools and information you can use in the day-to-day management of your health conditions.
Performing Postural Drainage and Chest Percussion
tests & procedures

You doctor may recommend one or more of the following tests to evaluate your condition.

Arterial Blood Gases
Chest X-Ray
Genetic Testing
Lung Function Tests
Sputum Culture
Stool Analysis for Cystic Fibrosis
Sweat Test

For other tests and diagnostic procedures use the section of this site called Medical Tests A to Z .

Lung Transplantation for Cystic Fibrosis


Influenza Virus Vaccine
Pneumococcal Polysaccharide Vaccine (Pneumovax)
Caregiver Tips
medication center
medication assistance

This section provides you with an alphabetical listing of more than 1,000 medications, including prescription drugs and those you can purchase over-the-counter. Just "click on" your medications to learn what they are used for, how to take them, special precautions, and some of the possible side effects. You can choose your medication by brand name or generic name.

Medications A-Z

If you are having difficulty paying for your medications you may qualify for financial assistance or free medications. Visit the Medication Assistance Center to learn about available medication and insurance programs.

Don't let financial problems stop you from getting the treatment you need; there are resources and organizations that may be able to help you.

additional resources

This listing provides you with Internet sites that are sponsored by government agencies or are well-known and credible national organizations.

American Lung Association

Boomer Esiason Foundation

Cystic Fibrosis Foundation

Cystic Fibrosis Research, Inc. (CFRI)


MEDLINEplus—Cystic Fibrosis

Surfing the Internet
When looking at Internet sites, remember that the information can be sponsored by anyone. Take into account the sponsoring group or individual when gathering information or help. Be especially careful about giving out personal or financial information.

Learn more about surfing the web:

Last modified on: 30 June 2015